Lhermitte – Duclos Disease in a Young Adult: Rare Entity
نویسندگان
چکیده مقاله:
Lhermitte - Duclos disease also called dysplastic gangliocytoma of cerebellum is an extremely rare cerebellar lesion which share features of both malformation and neoplasm. The usual presentation is of raised intracranial pressure along with cerebellar signs. We report a case of 23 year male who presented with headache & diplopia. MRI was suggestive of the diagnosis. Subtotal excision of the mass along with shunt drainage was performed. Post operative course was uneventful. Histopathological features confirmed the diagnosis.
منابع مشابه
lhermitte – duclos disease in a young adult: rare entity
lhermitte - duclos disease also called dysplastic gangliocytoma of cerebellum is an extremely rare cerebellar lesion which share features of both malformation and neoplasm. the usual presentation is of raised intracranial pressure along with cerebellar signs. we report a case of 23 year male who presented with headache & diplopia. mri was suggestive of the diagnosis. subtotal excision of th...
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Lhermitte-Duclos disease (LDD) is a benign neoplasm of posterior fossa, involving cerebellum. It is also known as dysplastic cerebellar gangliocytoma. It is not a true neoplasm but a hamartoma. It can be either isolated finding or associated with Cowden (multiple hamartoma syndrome). adults.
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Lhermitte-Duclos disease (dysplastic gangliocytoma of the cerebellum) is a rare benign cerebellar mass of unknown etiology which is characterized by enlargement of the cerebellar folia. Despite the controversy regarding its pathogenesis, imaging and histopathological findings are rather typical. A 17-year-old female presented with a 2-year history of progressive headaches and gait imbalance. Cr...
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عنوان ژورنال
دوره 8 شماره 3
صفحات 194- 198
تاریخ انتشار 2013-07-01
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